Craniosynostosis is defined as the premature fusion of one or more cranial sutures. The condition can present as an isolated defect or as a part of a syndrome with other anomalies (American Family Physician 69:2863-2870, 2004). Premature fusion of the metopic suture is relatively rare with an incidence of 7 per 2500 births (Child’s Nervous System 21:392-398, 2005). Thorough preoperative planning and patient education are essential for an ideal aesthetic result and patient satisfaction. A variety of surgical techniques have been described, depending on the age of the patient and the severity of the deformity. These have varied from simple suturectomies to extensive calvarial vault remodeling. More recently, endoscopically assisted procedures and distraction osteogenesis followed by helmet therapy have gained considerable popularity.