Aim: The chapter reviews the incidence, diagnosis, and surgical management of patients with cervical agenesis and dysgenesis, with or without vaginal aplasia. The various treatment options are reviewed, taking into account the specific anatomical characteristics of the defect. Brief description of the reviewed data: The different surgical techniques for cervical agenesis and dysgenesis, including hysterectomy, coring of the cervix, utero- vaginal anastomosis, along with the use of grafts, are evaluated, along with their risks and benefits.Clinical implications: New surgical techniques are being improved upon to optimize the outcome of patients with this rare congenital anomaly and preserve uterine integrity.Open Issues for further research: Despite case series of patients and their surgical outcomes, this remains a rare disorder with no randomized trials to support best case management. There is also limited research regarding pregnancy outcomes in patients with good surgical outcomes.
